Cystic fibrosis is a genetic disease, most common among Caucasians, that affects the lungs and digestive system. The defective gene, CFTR, responsible for cystic fibrosis leads to a production of thick, sticky mucus that clogs the lungs and obstructs the pancreas. This can make breathing difficult since the thick, sticky mucus makes it difficult to cough out of the lungs, which leads to severe lung infections. The mucus prevents proteins needed for digestion from reaching the intestines, which decreases the body’s ability to absorb nutrients from food, leading to malnutrition.
- Kitabis® Pak
- TOBI™ Podhaler™
- Inhaled hypertonic saline 7% nebulization solution
Pancreatic Enzyme Replacement Therapy & fat soluble vitamin A,D,E,K supplements
- Nebulizers turn liquid solutions into a mist which you inhale via mask. Oftentimes, Cystic fibrosis patients require a specific compressor and nebulizer to achieve an optimal outcome.
- Always clean and disinfect your nebulizer to minimize the risk of infection.